Electrophoresis of glucocerebrosidase from normal and Gaucher disease fibroblasts
- PMID: 484554
- PMCID: PMC1685886
Electrophoresis of glucocerebrosidase from normal and Gaucher disease fibroblasts
Abstract
A polyacrylamide gel electrophoresis system for glucocerebrosidase has been developed. This method was used to characterize the glucocerebrosidase activity of normal and Gaucher disease fibroblasts; the residual glucocerebrosidase activity in adult Gaucher disease fibroblasts co-migrates with the activity from normal fibroblasts.
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