Diencephalic syndrome of infantile emaciation. Analysis of literature and report of further 3 cases
- PMID: 5034666
- PMCID: PMC1648126
- DOI: 10.1136/adc.47.253.338
Diencephalic syndrome of infantile emaciation. Analysis of literature and report of further 3 cases
Abstract
Three children with diencephalic tumours are described, and an analysis of 45 cases from the literature together with our own 3 is presented. Boys are affected more frequently than girls (1·8:1) and the onset is during the first 12 months of life in 92% of cases. The main clinical features are emaciation, overactivity, pleasant disposition, and above-average height. The natural course of the disease is variable. Treatment is by radiotherapy. Operative intervention, except to relieve intracranial hypertension, is not usually indicated.
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