Lethal complications of the Ehlers-Danlos syndrome
- PMID: 5673215
- PMCID: PMC1986531
- DOI: 10.1136/bmj.3.5619.656
Lethal complications of the Ehlers-Danlos syndrome
Abstract
Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome.