doi: 10.1016/s0022-5347(17)55401-4.
Neoplasms associated with hemihypertophy, Beckwith-Wiedemann syndrome and aniridia
- PMID: 6249939
- DOI: 10.1016/s0022-5347(17)55401-4
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Neoplasms associated with hemihypertophy, Beckwith-Wiedemann syndrome and aniridia
J Urol.
1980 Aug.
Abstract
Hemihypertophy and the Beckwith-Wiedemann syndrome are associated with Wilms tumor and adrenocortical carcinoma. These conditions also have a relationship with nodular renal blastema, nephroblastomatosis and adrenocortical adenomas, all of which are pre-malignant lesions. children with aniridia also are predisposed to development of Wilms tumors.
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