The heart in Friedreich's ataxia
- PMID: 6663313
- PMCID: PMC491781
- DOI: 10.1136/jnnp.46.12.1138
The heart in Friedreich's ataxia
Abstract
Seventeen patients with Freidreich's ataxia were investigated for cardiac abnormalities using non-invasive methods. Clinical examination, routine chest radiographs and electrocardiograms were a poor guide to underlying heart involvement but using continuous ambulatory electrocardiographic monitoring, echocardiography and isotope ventriculography all patients were found to have abnormalities, even when the neurological signs were minimal.
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