[Case of three peculiar tumors of gastric epithelioid leiomyosarcoma, retroperitoneal paraganglioma and pulmonary chondroma]

Abstract

A 27-year-old woman with an unusual combination of three independent tumors, gastric epithelioid leiomyosarcoma, retroperitoneal paraganglioma and pulmonary chondroma is reported. There are 15 similar cases collected by Carney (1979) from the literature; ours is the first Japanese case. Patients with this tumor triad tend to be young females, all were of blood group A. The prognosis of these patients is generally good without associated systemic hypertension. Our patient is well 18 months after surgical removal of the three tumors.