Primary immunodeficiency disorders in Sweden: cases among children, 1974-1979
- PMID: 6978347
- DOI: 10.1007/BF00916891
Primary immunodeficiency disorders in Sweden: cases among children, 1974-1979
Abstract
A nationwide survey of symptomatic primary immunodeficiency disorders in children in Sweden during the 6-year period 1974-1979 resulted in 201 reported cases. The reported data for 174 children were analyzed. Antibody deficiencies were the most frequent (45.0%), followed by phagocytic disorders (22.0%) and combined T- and B-cell disorders (20.8%). Thirty-two children (18.4%) died, with the highest mortality for combined T- and B-cell defects. The sex ratio for all disorders was 2:1 for boys:girls. Neutropenia was significantly more common in the northern part of Sweden.