Review
doi: 10.1007/BF00287042.
XY females with enzyme deficiencies of steroid metabolism. A brief review
- PMID: 6989745
- DOI: 10.1007/BF00287042
Item in Clipboard
Review
XY females with enzyme deficiencies of steroid metabolism. A brief review
Hum Genet.
1980.
Abstract
The literature on XY females with enzyme deficiencies (17 alpha-hydroxylase, 17 beta-reductase and 17, 20-desmolase) is reviewed. The main features of these individuals are briefly compared with those of XY females with pure gonadal dysgenesis and with testicular feminization.
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