[Hemophilic pseudotumors]

Abstract

A review of the literature was made with special interest in morphology, pathogenesis and treatment of hemophilic pseudotumors. 110 reports of hemophilic pseudotumors were evaluated and compared with 25 own cases. The separation according to the inflicted site and the primarily involved anatomical structure revealed three types of hemophilic pseudotumors: 1. Intramuscular hematomas which enter secondarily into the periosteum. a) In the diaphyses of long tubular bones (femur 49, lower leg 14, humerus 4, forearm 2). b) In the iliac bone (37). 2. Intraspongious cysts in short cancellous bones (calcaneus 14, talus 5, scapula 3). 3. Direct subperiostal hematomas in the phalanges and metacarpals in the hand (thumb 5, finger 1, metacarpal 1). Concerning treatment, there is to state, that in general a conservative approach (substitution of the missing clotting factor and immobilization) is promising. The operative indications are demonstrated and determined, using case reports.