[Pulmonary involvement in Schonlein-Henoch's purpura]

Abstract

A case of vascular purpura was observed in a 8 year-old girl. The clinical symptoms and pathological findings in kidneys and skin were compatible with Henoch-Schonlein syndrome. She presented with dyspnea and frequent acute pulmonary failure and the chest X-ray showed changing pulmonary infiltration. Despite treatment with corti-costeroids and cyclophosphamide, she died after 16 months. Pulmonary alveolar oedema, focal interstitial fibrosis and arterial fibrinoid thrombosis were found at autopsy. There was neither collagen lesion, nor fibrinoid necrosis.