Friedreich's ataxia: I. Normal pyruvate dehydrogenase complex activity in platelets
- PMID: 727741
- DOI: 10.1002/ana.410040412
Friedreich's ataxia: I. Normal pyruvate dehydrogenase complex activity in platelets
Similar articles
-
Serum and platelet lipoamide dehydrogenase in Friedreich's ataxia.Can J Neurol Sci. 1978 Feb;5(1):111-4. Can J Neurol Sci. 1978. PMID: 647485
-
Normal pyruvate dehydrogenase complex activity in patients with Friedreich's ataxia.Ann Neurol. 1980 Dec;8(6):636-9. doi: 10.1002/ana.410080618. Ann Neurol. 1980. PMID: 7212654 No abstract available.
-
Pyruvate dehydrogenase complex in Friedreich's ataxia.Adv Neurol. 1978;21:203-17. Adv Neurol. 1978. PMID: 367116 Review. No abstract available.
-
Active pyruvate dehydrogenase in platelets from Friedreich's ataxia patients.Can J Neurol Sci. 1980 Nov;7(4):417-9. doi: 10.1017/s0317167100022988. Can J Neurol Sci. 1980. PMID: 7214256
-
Evidence for a primary defect of lipoamide dehydrogenase in Friedreich's ataxia.Adv Neurol. 1978;21:163-80. Adv Neurol. 1978. PMID: 104555 Review.
Cited by
-
Activities of branched-chain 2-oxo acid dehydrogenase and its components in skin fibroblasts from normal and classical-maple-syrup-urine-disease subjects.Biochem J. 1981 Oct 15;200(1):59-67. doi: 10.1042/bj2000059. Biochem J. 1981. PMID: 6895847 Free PMC article.
-
Induction of the branched-chain 2-oxo acid dehydrogenase complex in 3T3-L1 adipocytes during differentiation.Biochem J. 1983 Jul 15;214(1):177-81. doi: 10.1042/bj2140177. Biochem J. 1983. PMID: 6615463 Free PMC article.
-
Mitochondrial enzymes in hereditary ataxias.Metab Brain Dis. 1988 Jun;3(2):151-60. doi: 10.1007/BF01001015. Metab Brain Dis. 1988. PMID: 3185426
-
Muscle biochemistry in thiamin-responsive anaemia.J Inherit Metab Dis. 1997 Jul;20(3):404-6. doi: 10.1023/a:1005302717117. J Inherit Metab Dis. 1997. PMID: 9266367 No abstract available.
-
A familial progressive neurodegenerative disease with 2-oxoglutaric aciduria.Eur J Pediatr. 1982 Feb;138(1):32-7. doi: 10.1007/BF00442325. Eur J Pediatr. 1982. PMID: 7075624
Publication types
MeSH terms
Substances
LinkOut - more resources
Full Text Sources