Eosinophilic fasciitis: report of a case with features of connective tissue diseases

Abstract

A patient suffering from eosinophilic facsiitis is described and the literature reviewed. The original description of eosinophilic fasciitis was that of a benign scleroderma-like disease with eosinophilia, hypergammaglobulinemia and diffuse thickening and inflammation of the fascia and subcutaneous tissue. Our patient like a few others, presented additional findings, namely, Raynaud's phenomenon and mild myhositis. She is the first patient described with Sjögren's syndrome. It is important that eosinophilic faciitis be recognized clinically because it seems to be a benign and treatable entity.