Total anomalous pulmonary venous connection in adults--a surgical review

Abstract

The authors report a case of surgical repair of total anomalous pulmonary venous connection in a 36-year-old male. This is a very rare disease in adulthood since over 80% of the infants die before one year of age. Fifty-two surgical cases were previously reported in the literature. An extensive review of these cases is presented. Surgery is the only treatment and offers excellent short- and long-term results.