Measurements of uridine diphosphate glucose and uridine diphosphate galactose--an appraisal
- PMID: 7671969
- DOI: 10.1007/BF02143807
Measurements of uridine diphosphate glucose and uridine diphosphate galactose--an appraisal
Abstract
The recent disproof of a major deficiency of uridine diphosphate galactose in galactosemia should not lead investigators to assume either that enzymatic methods are unreliable for uridine sugar assays or that a defect in galactosylation in galactosemia has been excluded.
Similar articles
-
Uridine diphosphate glucose and uridine diphosphate galactose in galactosemia.J Pediatr. 1991 Aug;119(2):329-31. doi: 10.1016/s0022-3476(05)80758-9. J Pediatr. 1991. PMID: 1861224 No abstract available.
-
Uridine diphosphate glucose and uridine diphosphate galactose in galactosemia.J Pediatr. 1990 Nov;117(5):838-42. doi: 10.1016/s0022-3476(05)83362-1. J Pediatr. 1990. PMID: 2231224 No abstract available.
-
Galactosemia: the uridine diphosphate galactose deficiency-uridine treatment controversy.J Pediatr. 1993 Dec;123(6):1009-14. doi: 10.1016/s0022-3476(05)80404-4. J Pediatr. 1993. PMID: 8229508 Review. No abstract available.
-
Estimates of uridine diphosphate hexoses in erythrocytes: implications for galactosemia.J Pediatr. 1993 Feb;122(2):257-9. doi: 10.1016/s0022-3476(06)80127-7. J Pediatr. 1993. PMID: 8429444
-
Defective galactosylation in galactosemia: is low cell UDPgalactose an explanation?Eur J Pediatr. 1995;154(7 Suppl 2):S65-71. doi: 10.1007/BF02143806. Eur J Pediatr. 1995. PMID: 7671968 Review.
Cited by
-
Galactosaemia: pathogenesis and treatment.J Inherit Metab Dis. 1996;19(1):3-7. doi: 10.1007/BF01799341. J Inherit Metab Dis. 1996. PMID: 8830174 Review. No abstract available.