Review
Malignancy in Maffucci's syndrome
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- PMID: 7712654
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Review
Malignancy in Maffucci's syndrome
Dermatol Clin.
1995 Jan.
Abstract
Maffucci's syndrome is characterized by multiple enchondromas and subcutaneous hemangiomas. These tumors typically present in early childhood and may lead to significant skeletal deformities. Malignant transformations are a common feature of this syndrome and have been reported in approximately 30% of reported cases, with chondrosarcomas being the most common.
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