Review
Multiple endocrine neoplasia 2B (MEN 2B)/MEN 3
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- PMID: 7712657
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Review
Multiple endocrine neoplasia 2B (MEN 2B)/MEN 3
Dermatol Clin.
1995 Jan.
Abstract
Multiple endocrine neoplasia type 2B/3 is characterized by multiple mucosal neuromas, a marfanoid appearance, medullary thyroid carcinoma, pheochromocytoma, gastrointestinal ganglioneuromatosis, and thickened corneal nerves. This rare syndrome is inherited in an autosomal dominant pattern. Early recognition followed by appropriate screening and treatment can be life-saving.
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