[Pseudomyxoma peritonei associated with appendiceal mucinous cystadenoma. Report of a case and review of the literature]

Abstract

Mucinous cystadenoma of the appendix is a rare entity. Its incidence is low, between 0.1 and 0.3%. Constitutes are found incidentally al surgery and is generally asymptomatic. We present a case of a 60 years old woman which was complicated by a pseudomyxoma peritonei, idiopathic ulcerative rectocolitis and infiltration of the muscular layer of the colon sigmoid wall with poorly differentiated adenocarcinoma. We reviewed the literature, emphasize modern concepts about its terminology and its possible pathogenesis.