Dermatomyositis treated with high-dose intravenous immunoglobulins and associated with panniculitis
- PMID: 8565257
- DOI: 10.1111/j.1365-2230.1995.tb02675.x
Dermatomyositis treated with high-dose intravenous immunoglobulins and associated with panniculitis
Abstract
Polymyositis and dermatomyositis are idiopathic inflammatory myopathies characterized by subacute symmetrical weakness of proximal limb and trunk muscles. Dermatomyositis is distinguished from polymyositis by the presence of rash. We describe an adult patient with treatment-resistant childhood-type dermatomyositis who made a good response to high dose intravenous immunoglobulins. Additionally, there was evidence of panniculitis which is an unusual histopathological finding in dermatomyositis.
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