doi: 10.1093/ajcn/30.7.1153.
Nutritional management of the female with phenylketonuria during pregnancy
- PMID: 879079
- DOI: 10.1093/ajcn/30.7.1153
Item in Clipboard
Nutritional management of the female with phenylketonuria during pregnancy
Am J Clin Nutr.
1977 Jul.
Abstract
This paper discusses a rational approach to appropriate nutritional management of the pregnant woman with phenylketonuria (PKU). Special food items, including new formulas and low-phenylalanine products, as well as allowable nutral foods are described. Particular emphasis is placed on the nutritional adequacy of this PKU diet during pregnancy. Such a diet should be palatable and tolerated well and should also take into consideration important economic, cultural, and psychological aspects. Clinics caring for PKU individuals should be so prepared because many otheir females are approaching childbearing age.
Similar articles
-
Timing of strict diet in relation to fetal damage in maternal phenylketonuria. An international collaborative study by the MRC/DHSS Phenylketonuria Register.Lancet. 1987 Oct 24;2(8565):927-30. doi: 10.1016/s0140-6736(87)91418-8. Lancet. 1987. PMID: 2889860
-
Maternal phenylketonuria: abnormal baby despite low phenylalanine diet during pregnancy.Arch Dis Child. 1980 Aug;55(8):634-7. doi: 10.1136/adc.55.8.634. Arch Dis Child. 1980. PMID: 7436520 Free PMC article.
-
Maternal phenylketonuria. Review with emphasis on pathogenesis.Enzyme. 1987;38(1-4):312-20. Enzyme. 1987. PMID: 3326736 Review.
-
Maternal phenylketonuria.Postgrad Med J. 1989;65 Suppl 2:S10-20. Postgrad Med J. 1989. PMID: 2622813
-
Maternal phenylketonuria: an international study.Mol Genet Metab. 2000 Sep-Oct;71(1-2):233-9. doi: 10.1006/mgme.2000.3038. Mol Genet Metab. 2000. PMID: 11001815 Review.
Cited by
-
Maternal phenylketonuria.Ir J Med Sci. 1979 Dec;148(1):310. doi: 10.1007/BF02938105. Ir J Med Sci. 1979. PMID: 27517443
-
Prevention of mental retardation in offspring of hyperphenylalaninemic mothers.Am J Public Health. 1982 Dec;72(12):1386-90. doi: 10.2105/ajph.72.12.1386. Am J Public Health. 1982. PMID: 7137436 Free PMC article.
-
Diet, genetics, and mental retardation interaction between phenylketonuric heterozygous mother and fetus to produce nonspecific diminution of IQ: evidence in support of the justification hypothesis.Proc Natl Acad Sci U S A. 1978 Mar;75(3):1562-6. doi: 10.1073/pnas.75.3.1562. Proc Natl Acad Sci U S A. 1978. PMID: 274741 Free PMC article.
-
Management of maternal phenylketonuria: an emerging clinical problem.Br Med J. 1979 May 26;1(6175):1383-7. doi: 10.1136/bmj.1.6175.1383. Br Med J. 1979. PMID: 445095 Free PMC article.
-
[Singleton and twin pregnancies of PKU patients - individual variability of phenylalanine tolerance: experience of a single treatment center (Preliminary report)].Dev Period Med. 2017;21(4):344-360. doi: 10.34763/devperiodmed.20172104.344360. Dev Period Med. 2017. PMID: 29291362 Free PMC article. Polish.