Lymphangiomyomatosis with chylous ascites: treatment with dietary fat restriction and medium chain triglycerides
- PMID: 890669
- DOI: 10.1002/1097-0142(197708)40:2<895::aid-cncr2820400245>3.0.co;2-8
Lymphangiomyomatosis with chylous ascites: treatment with dietary fat restriction and medium chain triglycerides
Abstract
Lymphangiomyomyoma is a tumor of lymphatic channels and lymph nodes, clinically manifested by recurrent chylous pleural effusions and ascites. The disease is usually progressive and unresponsive to surgery, chemotherapy, or irradiation. A case of lymphangiomyomatosis in a 24-year-old woman who presented with chylous ascites is described. The patient was treated with dietary fat restriction supplemented with medium chain triglycerides and has remained free of recurrent effusions for 2 years.
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