Meleda disease: report of two cases investigated by electron microscopy
- PMID: 8993971
- DOI: 10.1159/000246295
Meleda disease: report of two cases investigated by electron microscopy
Abstract
We report 2 cases of clinically typical Meleda disease in a family from Herzegovina. Electron microscopy did not reveal major ultrastructural anomalies of keratinization; however, the transition from stratum granulosum to stratum corneum appeared to occur less abruptly than normally by a stepwise process suggesting a slowing down of terminal cornification.
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