Short colon malformation with imperforate anus

Abstract

Ten cases of a rare high anorectal malformation associated with short colon are presented. The significance of a large gas fluid level (occupying more than half of the abdominal cavity on invertogram) is stressed for pre-operative diagnosis. Terminal colostomy or ileostomy with disconnection of colo-vesical/colo-vaginal fistula has been considered the only adequate therapy. Associated congenital malformations have been responsible for high mortality in these patients.