Use of saponin-permeabilized muscle fibers for the diagnosis of mitochondrial diseases
- PMID: 9568252
- DOI: 10.1002/biof.5520070312
Use of saponin-permeabilized muscle fibers for the diagnosis of mitochondrial diseases
Similar articles
-
Polarographic studies of saponin-skinned muscle fibres in patients with mitochondrial myopathies.J Inherit Metab Dis. 1994;17(3):307-10. doi: 10.1007/BF00711815. J Inherit Metab Dis. 1994. PMID: 7807939 No abstract available.
-
Functional characterization of mitochondrial oxidative phosphorylation in saponin-skinned human muscle fibers.Biochim Biophys Acta. 1993 Aug 16;1144(1):46-53. doi: 10.1016/0005-2728(93)90029-f. Biochim Biophys Acta. 1993. PMID: 8347661
-
Familial myopathy with conspicuous depletion of mitochondria in muscle fibers: a morphologically distinct disease.Neuromuscul Disord. 1995 Mar;5(2):139-44. doi: 10.1016/0960-8966(94)00039-c. Neuromuscul Disord. 1995. PMID: 7767093
-
[Mitochondriopathies].Rev Neurol. 2003 Oct 16-31;37(8):775-9. Rev Neurol. 2003. PMID: 14593640 Review. Spanish.
-
Diagnosis of mitochondrial myopathies.Mol Genet Metab. 2013 Sep-Oct;110(1-2):35-41. doi: 10.1016/j.ymgme.2013.07.007. Epub 2013 Jul 17. Mol Genet Metab. 2013. PMID: 23911206 Review.
Cited by
-
Blood-based bioenergetics: An emerging translational and clinical tool.Mol Aspects Med. 2020 Feb;71:100835. doi: 10.1016/j.mam.2019.100835. Epub 2019 Dec 18. Mol Aspects Med. 2020. PMID: 31864667 Free PMC article. Review.
-
Analysis of Mitochondrial Function, Structure, and Intracellular Organization In Situ in Cardiomyocytes and Skeletal Muscles.Int J Mol Sci. 2022 Feb 18;23(4):2252. doi: 10.3390/ijms23042252. Int J Mol Sci. 2022. PMID: 35216368 Free PMC article. Review.
-
Respirometric oxidative phosphorylation assessment in saponin-permeabilized cardiac fibers.J Vis Exp. 2011 Feb 28;(48):2431. doi: 10.3791/2431. J Vis Exp. 2011. PMID: 21403632 Free PMC article.
-
Short-term caloric restriction, resveratrol, or combined treatment regimens initiated in late-life alter mitochondrial protein expression profiles in a fiber-type specific manner in aged animals.Exp Gerontol. 2013 Sep;48(9):858-68. doi: 10.1016/j.exger.2013.05.061. Epub 2013 Jun 7. Exp Gerontol. 2013. PMID: 23747682 Free PMC article.
Publication types
MeSH terms
Substances
LinkOut - more resources
Full Text Sources
Other Literature Sources