Progressive encephalomyelitis with rigidity
- PMID: 963529
- DOI: 10.1093/brain/99.1.27
Progressive encephalomyelitis with rigidity
Abstract
Two cases of encephalomyelitis are described in which the major clinical manifestation was muscular rigidity and stimulus-sensitive muscular spasms. It is suggested, from pathological evidence, that this rigidity was of spinal origin, and that this disorder is a rare but recognizable entity. Comparison is made with previously reported cases of rigidity of spinal origin, including encephalitis lethargica, and with 'subacute myoclonic spinal neuronitis' and the 'stiff man syndrome.'
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