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Page 1
Orbital/ocular inflammatory involvement in VEXAS syndrome: Data from the international AIDA network VEXAS registry.
Vitale A, Caggiano V, Martin-Nares E, Frassi M, Dagna L, Hissaria P, Sfriso P, Hernández-Rodríguez J, Ruiz-Irastorza G, Monti S, Tufan A, Piga M, Giardini HAM, Lopalco G, Viapiana O, De Paulis A, Triggianese P, Vitetta R, de-la-Torre A, Fonollosa A, Caroni F, Sota J, Conticini E, Sbalchiero J, Renieri A, Casamassima G, Wiesik-Szewczyk E, Yildirim D, Hinojosa-Azaola A, Crisafulli F, Franceschini F, Campochiaro C, Tomelleri A, Callisto A, Beecher M, Bindoli S, Baggio C, Gómez-Caverzaschi V, Pelegrín L, Soto-Peleteiro A, Milanesi A, Vasi I, Cauli A, Antonelli IPB, Iannone F, Bixio R, Casa FD, Mormile I, Gurnari C, Fiorenza A, Mejia-Salgado G, Kawakami-Campos PA, Ragab G, Ciccia F, Ruscitti P, Bocchia M, Balistreri A, Tosi GM, Frediani B, Cantarini L, Fabiani C. Vitale A, et al. Among authors: frassi m. Semin Arthritis Rheum. 2024 Jun;66:152430. doi: 10.1016/j.semarthrit.2024.152430. Epub 2024 Mar 18. Semin Arthritis Rheum. 2024. PMID: 38554594 Free article.
American College of Rheumatology Guidance Statement for Diagnosis and Management of VEXAS Developed by the International VEXAS Working Group Expert Panel.
Mekinian AM, Georgin-Lavaille S, Ferrada MA, Savic S, Koster MJ, Kosmider O, Comont T, Heilblig M, Arostegui JI, Bosco A, Bourguiba R, Calvo KR, Cargo C, Cattaneo C, Chasset F, Coelho H, Campochiaro C, Crisafulli F, Ducharme-Benard S, Faria R, Franceschini F, Frassi M, Groarke EM, Gurnari C, Hakobyan Y, Jamilloux Y, Jurcut C, Kirino Y, Kulasekararaj A, Kunimoto H, Madigan LM, Mann HF, Marvisi C, Milchert M, Morais S, Sockel K, Muratore F, Nakajima H, Patnaik MM, Regadas L, Robin M, Rutgers A, Salvarani C, Sammel AM, Seebach J, Sujobert P, Tomelleri A, Urbanski G, Vandergheynst F, Vieira R, Viswanatha DS, Więsik-Szewczyk E, Diral E, Terrier B, Patel BA, Fenaux P, Grayson PC, Beck DB; International VEXAS working group, and with endorsement of EuroBloodNet, the European Reference Network in Rare Hematological Diseases. Mekinian AM, et al. Among authors: frassi m. Arthritis Rheumatol. 2025 Aug 11. doi: 10.1002/art.43287. Online ahead of print. Arthritis Rheumatol. 2025. PMID: 40787890
Erythroid-stimulating agents in VEXAS syndrome: A retrospective study from an Italian multicentre cohort.
Diral E, Campochiaro C, Furnari G, Moretti F, Ferrari J, Elena C, Battipaglia G, Barbato S, Vitale A, Frigeni M, Crisafulli F, Frassi M, Papayannidis C, Romagnoli AD, Cattaneo C, D'Ambrosio A, Morsia E, Musto P, Rivoli G, Dragani ME, Toffalori C, Bergonzi GM, Scorpio G, Tomelleri A, Voso MT, Gurnari C, Vago L, Dagna L, Ciceri F. Diral E, et al. Among authors: frassi m. Br J Haematol. 2025 May 13;207(1):273-7. doi: 10.1111/bjh.20157. Online ahead of print. Br J Haematol. 2025. PMID: 40364459 Free PMC article. No abstract available.
Still's disease continuum from childhood to elderly: data from the international AIDA Network Still's disease registry.
Vitale A, Caggiano V, Lopalco G, Mayrink Giardini HA, Ciccia F, Almaghlouth IA, Ruscitti P, Sfikakis PP, Tufan A, Dagna L, Giacomelli R, Hinojosa-Azaola A, Ragab G, Direskeneli H, Fotis L, Sota J, Iannone F, Morrone M, de Brito Antonelli IP, Dagostin MA, Iacono D, Patrone M, Asfina K, Alanazi F, Di Cola I, Gaggiano C, Tektonidou MG, Kardas RC, Kucuk H, Campochiaro C, Tomelleri A, Navarini L, Berardicurti O, Martín-Nares E, Torres-Ruiz J, Mahmoud AAA, Alibaz-Oner F, Kourtesi K, Tarsia M, Sfriso P, Makowska J, Govoni M, La Torre F, Maggio MC, Monti S, Del Giudice E, Emmi G, Bartoloni E, Hernández-Rodríguez J, Gómez-Caverzaschi V, Maier A, Simonini G, Iagnocco A, Conti G, Olivieri AN, De Paulis A, Lo Gullo A, Viapiana O, Wiesik-Szewczyk E, Erten S, Ogunjimi B, Carubbi F, Tharwat S, Laskari K, Costi S, Triggianese P, Karamanakos A, Conforti A, Frassi M, Sebastiani GD, Gidaro A, Mauro A, Balistreri A, Fabiani C, Frediani B, Cantarini L. Vitale A, et al. Among authors: frassi m. RMD Open. 2023 Dec 1;9(4):e003578. doi: 10.1136/rmdopen-2023-003578. RMD Open. 2023. PMID: 38053457 Free PMC article.
Diagnostic capabilities, clinical features, and longitudinal UBA1 clonal dynamics of a nationwide VEXAS cohort.
Gurnari C, Pascale MR, Vitale A, Diral E, Tomelleri A, Galossi E, Falconi G, Bruno A, Crisafulli F, Frassi M, Cattaneo C, Bertoli D, Bernardi M, Condorelli A, Morsia E, Poloni A, Crisà E, Caravelli D, Triggianese P, Brussino L, Battipaglia G, Bindoli S, Sfriso P, Caroni F, Dragani M, Mallegni F, Pilo F, Firinu D, Curti A, Papayannidis C, Olivieri A, Kordasti S, Albano F, Pane F, Musto P, Bocchia M, Lugli E, Breccia M, Frigeni M, Dagna L, Greco R, Franceschini F, Campochiaro C, Cantarini L, Voso MT. Gurnari C, et al. Among authors: frassi m. Am J Hematol. 2024 Feb;99(2):254-262. doi: 10.1002/ajh.27169. Epub 2023 Dec 18. Am J Hematol. 2024. PMID: 38108611 Free article.
Clinical and laboratory features associated with macrophage activation syndrome in Still's disease: data from the international AIDA Network Still's Disease Registry.
Triggianese P, Vitale A, Lopalco G, Mayrink Giardini HA, Ciccia F, Al-Maghlouth I, Ruscitti P, Sfikakis PP, Iannone F, de Brito Antonelli IP, Patrone M, Asfina KN, Di Cola I, Laskari K, Gaggiano C, Tufan A, Sfriso P, Dagna L, Giacomelli R, Hinojosa-Azaola A, Ragab G, Fotis L, Direskeneli H, Spedicato V, Dagostin MA, Iacono D, Ali HH, Cipriani P, Sota J, Kardas RC, Bindoli S, Campochiaro C, Navarini L, Gentileschi S, Martín-Nares E, Torres-Ruiz J, Saad MA, Kourtesi K, Alibaz-Oner F, Sevik G, Iagnocco A, Makowska J, Govoni M, Monti S, Maggio MC, La Torre F, Del Giudice E, Hernández-Rodríguez J, Bartoloni E, Emmi G, Chimenti MS, Maier A, Simonini G, Conti G, Olivieri AN, Tarsia M, De Paulis A, Lo Gullo A, Więsik-Szewczyk E, Viapiana O, Ogunjimi B, Tharwat S, Erten S, Nuzzolese R, Karamanakos A, Frassi M, Conforti A, Caggiano V, Marino A, Sebastiani GD, Gidaro A, Tombetti E, Carubbi F, Rubegni G, Cartocci A, Balistreri A, Fabiani C, Frediani B, Cantarini L. Triggianese P, et al. Among authors: frassi m. Intern Emerg Med. 2023 Nov;18(8):2231-2243. doi: 10.1007/s11739-023-03408-3. Epub 2023 Oct 12. Intern Emerg Med. 2023. PMID: 37828268 Free PMC article.
Efficacy of canakinumab in patients with Still's disease across different lines of biologic therapy: real-life data from the International AIDA Network Registry for Still's Disease.
Vitale A, Caggiano V, Sfikakis PP, Dagna L, Lopalco G, Ragab G, La Torre F, Almaghlouth IA, Maggio MC, Sota J, Tufan A, Hinojosa-Azaola A, Iannone F, Loconte R, Laskari K, Direskeneli H, Ruscitti P, Morrone M, Mayrink Giardini HA, Panagiotopoulos A, Di Cola I, Martín-Nares E, Monti S, De Stefano L, Kardas RC, Duran R, Campochiaro C, Tomelleri A, Alabdulkareem AM, Gaggiano C, Tarsia M, Bartoloni E, Romeo M, Hussein MA, Laymouna AH, Parente de Brito Antonelli I, Dagostin MA, Fotis L, Bindoli S, Navarini L, Alibaz-Oner F, Sevik G, Frassi M, Ciccia F, Iacono D, Crisafulli F, Portincasa P, Jaber N, Kawakami-Campos PA, Wiesik-Szewczyk E, Iagnocco A, Simonini G, Sfriso P, Balistreri A, Giacomelli R, Conti G, Frediani B, Fabiani C, Cantarini L. Vitale A, et al. Among authors: frassi m. Front Med (Lausanne). 2023 Dec 12;10:1256243. doi: 10.3389/fmed.2023.1256243. eCollection 2023. Front Med (Lausanne). 2023. PMID: 38148914 Free PMC article.
Efficacy and safety of conventional disease-modifying antirheumatic drugs in VEXAS syndrome: real-world data from the international AIDA network.
Vitale A, Leone F, Caggiano V, Hinojosa-Azaola A, Martín-Nares E, Guaracha-Basañez GA, Torres-Ruiz J, Ayumi Kawakami-Campos P, Hissaria P, Callisto A, Beecher M, Dagna L, Tomelleri A, Campochiaro C, Frassi M, Crisafulli F, Franceschini F, Hernández-Rodríguez J, Gómez-Caverzaschi V, Araújo O, Sfriso P, Bindoli S, Baggio C, Sbalchiero J, Sota J, Tufan A, Vasi I, Piga M, Cauli A, D'Agostino MA, De Paulis A, Mormile I, Mayrink Giardini HA, Cordeiro RA, Gavioli F, Lopalco G, Iannone F, Montecucco C, Monti S, Ruiz-Irastorza G, Soto-Peleteiro A, Triggianese P, Gurnari C, Viapiana O, Bixio R, Vitetta R, Conticini E, La Torre F, Ragab G, Batu ED, González-García A, Peña-Rodríguez M, Bocchia M, Wiesik-Szewczyk E, Jahnz-Rózyk K, de-la-Torre A, Balistreri A, Frediani B, Fabiani C, Cantarini L. Vitale A, et al. Among authors: frassi m. Front Pharmacol. 2025 Mar 7;16:1539756. doi: 10.3389/fphar.2025.1539756. eCollection 2025. Front Pharmacol. 2025. PMID: 40124776 Free PMC article.
The clinical assessment of lung involvement in patients with Still's disease, results from the multicentre international AIDA Network Still's Disease Registry.
Ruscitti P, Vitale A, Di Cola I, Caggiano V, Palumbo P, Di Cesare E, Hinojosa-Azaola A, Torres-Ruiz J, Guaracha-Basañez GA, Martín-Nares E, Lopalco G, Morrone M, Iannone F, Giardini HAM, Cordeiro RA, de Brito Antonelli IP, Berardicurti O, Navarini L, Ciccia F, Visconti MC, Iacono D, Direskeneli H, Erten S, Yao H, Thabet M, Tharwat S, Ragab G, Gómez-Caverzaschi V, Sfikakis PP, Fotis L, La Torre F, Maier A, Karamanakos A, Almaghlouth IA, Frassi M, Tufan A, Govoni M, Sota J, Simonini G, Emmi G, Li Gobbi F, Parronchi P, Costi S, Sarzi-Puttini P, Opris-Belinski D, Sfriso P, Tarsia M, Maggio MC, Monti S, Gündüz ÖS, Rigante D, Bartoloni E, Verrecchia E, Iagnocco A, Viapiana O, Bargagli E, Batu ED, Sebastiani GD, Del Giudice E, Conti G, Breda L, Gidaro A, Gicchino MF, Gaggiano C, Brucato AL, Triggianese P, Makowska J, Carubbi F, Farina N, Guggino G, De Paulis A, Mazzei MA, Di Meglio N, Lo Gullo A, Conforti A, Ogunjimi B, Calabrese L, Rubegni P, Giardina A, Wiesik-Szewczyk E, Balistreri A, Fabiani C, Frediani B, Dagna L, Giacomelli R, Cantarini L. Ruscitti P, et al. Among authors: frassi m. Rheumatology (Oxford). 2025 Jan 20:keaf021. doi: 10.1093/rheumatology/keaf021. Online ahead of print. Rheumatology (Oxford). 2025. PMID: 39832276
82 results